The narrator is visiting an old friend who has written a letter speaking of his illness. As the narrator approaches the house, he describes its spooky, eerie feeling despite his attempt to divert the feeling. He eventually meets his oddly cheerful friend named Roderick Usher.
Usher has an illness that exists within his family. His sister, Madeline, eventually dies of this illness, leaving Usher stranger or even madder than before. This feeling begins to affect the narrator.
Usher and the narrator are caught in a spooky storm. They decide to read a book to suppress the uncanny feeling that arises. The events in the seemingly harmless book coincide with metal clanging of the door in the basement where Madeline is entombed.
User cracks. He begins to frantically talk about how he had known all along that they had entombed Lady Madeline alive. Near this moment, Lady Madeline and Roderick meet.
Lady Madeline reacts with anger and Roderick Usher succumbs to his greatest fear, a fear of fear. The sight of one another causes them both to tragically die.
The narrator fleas the scene. As he looks back, he notices the crack in the exterior wall of the house growing larger. The house of Usher falls.