The narrator arrives at the House of Usher. His friend, Roderick Usher wrote him an urgent letter asking him to go visit him because he was physically and mentally ill.
Roderick is very ill and the narrator notices that his friend is mentally unstable. To make matters worst, Roderick's sister, Madeline is dying. Once he believes she is dead, he keeps puts he body in a coffin and puts her in the dungeon's vault.
Days later on a stormy night, neither the narrator nor Roderick can sleep, they both keep hearing screeching noises, but ignore it and neither one of them talks about it. Roderick is really in bad shape because of his sister's death and his mental illness gets worse. The narrator tries to calm him down by reading to him and sharing their love for music.
The noises coming from the dungeon get louder and they hear a loud scream. Roderick flips out and confesses that he has been hearing the noises for days, but said nothing. He tells the narrator that he is afraid because he thinks that he buried his sister while she was still alive. All of a sudden, the door is pushed open and Madeline appears. She is covered in blood.
Madeline goes to Roderick and falls on him, Roderick is so frighten by what he saw that he falls down dead. The twins died in each others arms.
The narrator hears the house crashing down in the storm and runs out. As he is running away, he sees the house crumbling down and completely disappear into the dark lake.